Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer

Saumya Prakash Srivastava

doi:doi:10.11648/j.ajnhs.20210204.11

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Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer

Saumya Prakash Srivastava

Published in American Journal of Nursing and Health Sciences (Volume 2, Issue 4)

Received: 7 August 2021 Accepted: 21 August 2021 Published: 5 November 2021

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Abstract

Dermatofibrosarcoma Protuberans (DFSP) is a very uncommon type of skin cancer that begins in the connective tissues of skin and extend to nearby structures in the form of lump. The cause of cutaneous fibroids is unknown, although a suggested risk factor includes skin lesions at the affected site. DFSP tends to affect people between the age of 20 and 50, but it has been diagnosed in people of all ages. This case report describes a highly recurrent DFSP disease condition of 25 years old female, who got admitted in a tertiary care cancer centre with complaints of painless swelling in the back, fever, and loss of weight since last 1 month. Surgical history revealed three past surgical excisions of the mass over the same location. CT scan and tissue biopsy revealed recurrent Dermatofibrosarcoma protuberans. Initially, the patient was on imatinib 600 mg/PO/OD, after which there was a subjective decrease in size of mass. But as the patient was unable to tolerate high doses of imatinib, she then underwent wide local excision of the mass with split skin graft taken from right thigh under general anesthesia. Surgery was uneventful and she was discharged thereafter. As local recurrence is common, patients required close clinical follow-up after completing treatment.

Published in	American Journal of Nursing and Health Sciences (Volume 2, Issue 4)
DOI	10.11648/j.ajnhs.20210204.11
Page(s)	87-89
Creative Commons	This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.
Copyright	Copyright © The Author(s), 2021. Published by Science Publishing Group

Keywords

Dermatofibrosarcoma Protuberans, Surgical Excisions, Soft Tissue Sarcoma, Rare Cancers

References

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[5]	Al Barwani AS, Taif S, Al Mazrouai RA, Al Muzahmi KS, Alrawi A. Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor. 6: 16.
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[9]	Wiesmueller F, Agaimy A, Perrakis A, Arkudas A, Horch RE, Grützmann R, et al. Dermatofibrosarcoma protuberans: surgical management of a challenging mesenchymal tumor. World Journal of Surgical Oncology. 2019 May 28; 17 (1): 90.
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[12]	Chan IL, Carneiro S, Menezes M, Ramos-E-Silva S, Magalhães T, Cuzzi T, et al. Dermatofibrosarcoma protuberans: a case report. Case Rep Dermatol. 2014 May 9; 6 (2): 134–9.
[13]	Bhambri S, Desai A, Del Rosso J, Mobini N. Dermatofibrosarcoma protuberans: A case report and review of the literature. The Journal of clinical and aesthetic dermatology. 2008 May 1; 1: 34–6.
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[15]	Saiag P, Grob J-J, Lebbe C, Malvehy J, del Marmol V, Pehamberger H, et al. Diagnosis and treatment of dermatofibrosarcoma protuberans. European consensus-based interdisciplinary guideline. European Journal of Cancer. 2015 Nov 1; 51 (17): 2604–8.
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APA Style

Saumya Prakash Srivastava. (2021). Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer. American Journal of Nursing and Health Sciences, 2(4), 87-89. https://doi.org/10.11648/j.ajnhs.20210204.11

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ACS Style

Saumya Prakash Srivastava. Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer. Am. J. Nurs. Health Sci. 2021, 2(4), 87-89. doi: 10.11648/j.ajnhs.20210204.11

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AMA Style

Saumya Prakash Srivastava. Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer. Am J Nurs Health Sci. 2021;2(4):87-89. doi: 10.11648/j.ajnhs.20210204.11

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@article{10.11648/j.ajnhs.20210204.11,
  author = {Saumya Prakash Srivastava},
  title = {Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer},
  journal = {American Journal of Nursing and Health Sciences},
  volume = {2},
  number = {4},
  pages = {87-89},
  doi = {10.11648/j.ajnhs.20210204.11},
  url = {https://doi.org/10.11648/j.ajnhs.20210204.11},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajnhs.20210204.11},
  abstract = {Dermatofibrosarcoma Protuberans (DFSP) is a very uncommon type of skin cancer that begins in the connective tissues of skin and extend to nearby structures in the form of lump. The cause of cutaneous fibroids is unknown, although a suggested risk factor includes skin lesions at the affected site. DFSP tends to affect people between the age of 20 and 50, but it has been diagnosed in people of all ages. This case report describes a highly recurrent DFSP disease condition of 25 years old female, who got admitted in a tertiary care cancer centre with complaints of painless swelling in the back, fever, and loss of weight since last 1 month. Surgical history revealed three past surgical excisions of the mass over the same location. CT scan and tissue biopsy revealed recurrent Dermatofibrosarcoma protuberans. Initially, the patient was on imatinib 600 mg/PO/OD, after which there was a subjective decrease in size of mass. But as the patient was unable to tolerate high doses of imatinib, she then underwent wide local excision of the mass with split skin graft taken from right thigh under general anesthesia. Surgery was uneventful and she was discharged thereafter. As local recurrence is common, patients required close clinical follow-up after completing treatment.},
 year = {2021}
}

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TY - JOUR
T1 - Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer
AU - Saumya Prakash Srivastava
Y1 - 2021/11/05
PY - 2021
N1 - https://doi.org/10.11648/j.ajnhs.20210204.11
DO - 10.11648/j.ajnhs.20210204.11
T2 - American Journal of Nursing and Health Sciences
JF - American Journal of Nursing and Health Sciences
JO - American Journal of Nursing and Health Sciences
SP - 87
EP - 89
PB - Science Publishing Group
SN - 2994-7227
UR - https://doi.org/10.11648/j.ajnhs.20210204.11
AB - Dermatofibrosarcoma Protuberans (DFSP) is a very uncommon type of skin cancer that begins in the connective tissues of skin and extend to nearby structures in the form of lump. The cause of cutaneous fibroids is unknown, although a suggested risk factor includes skin lesions at the affected site. DFSP tends to affect people between the age of 20 and 50, but it has been diagnosed in people of all ages. This case report describes a highly recurrent DFSP disease condition of 25 years old female, who got admitted in a tertiary care cancer centre with complaints of painless swelling in the back, fever, and loss of weight since last 1 month. Surgical history revealed three past surgical excisions of the mass over the same location. CT scan and tissue biopsy revealed recurrent Dermatofibrosarcoma protuberans. Initially, the patient was on imatinib 600 mg/PO/OD, after which there was a subjective decrease in size of mass. But as the patient was unable to tolerate high doses of imatinib, she then underwent wide local excision of the mass with split skin graft taken from right thigh under general anesthesia. Surgery was uneventful and she was discharged thereafter. As local recurrence is common, patients required close clinical follow-up after completing treatment.
VL - 2
IS - 4
ER -

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Author Information

Saumya Prakash Srivastava

Vivekanand Polyclinic College of Nursing, Lucknow, India

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APA Style

Saumya Prakash Srivastava. (2021). Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer. American Journal of Nursing and Health Sciences, 2(4), 87-89. https://doi.org/10.11648/j.ajnhs.20210204.11

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ACS Style

Saumya Prakash Srivastava. Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer. Am. J. Nurs. Health Sci. 2021, 2(4), 87-89. doi: 10.11648/j.ajnhs.20210204.11

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AMA Style

Saumya Prakash Srivastava. Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer. Am J Nurs Health Sci. 2021;2(4):87-89. doi: 10.11648/j.ajnhs.20210204.11

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@article{10.11648/j.ajnhs.20210204.11,
  author = {Saumya Prakash Srivastava},
  title = {Dermatofibrosarcoma Protuberans (DFSP): An Uncommon Skin Cancer},
  journal = {American Journal of Nursing and Health Sciences},
  volume = {2},
  number = {4},
  pages = {87-89},
  doi = {10.11648/j.ajnhs.20210204.11},
  url = {https://doi.org/10.11648/j.ajnhs.20210204.11},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajnhs.20210204.11},
  abstract = {Dermatofibrosarcoma Protuberans (DFSP) is a very uncommon type of skin cancer that begins in the connective tissues of skin and extend to nearby structures in the form of lump. The cause of cutaneous fibroids is unknown, although a suggested risk factor includes skin lesions at the affected site. DFSP tends to affect people between the age of 20 and 50, but it has been diagnosed in people of all ages. This case report describes a highly recurrent DFSP disease condition of 25 years old female, who got admitted in a tertiary care cancer centre with complaints of painless swelling in the back, fever, and loss of weight since last 1 month. Surgical history revealed three past surgical excisions of the mass over the same location. CT scan and tissue biopsy revealed recurrent Dermatofibrosarcoma protuberans. Initially, the patient was on imatinib 600 mg/PO/OD, after which there was a subjective decrease in size of mass. But as the patient was unable to tolerate high doses of imatinib, she then underwent wide local excision of the mass with split skin graft taken from right thigh under general anesthesia. Surgery was uneventful and she was discharged thereafter. As local recurrence is common, patients required close clinical follow-up after completing treatment.},
 year = {2021}
}

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