A previously well young Filipino boy presented with prolonged recurrent left focal to bilateral seizure. He was born of a non-consanguineous marriage, home-delivered vaginally, full term with no perinatal complications. He had normal growth and developmental milestones until at the age of 7 months when he developed febrile status epilepticus. Since then, he was left with residual left hemiplegia, dysarthria, cognitive delay and recurrent seizures occurring twice daily. He was poorly compliant on multiple anti-seizure medications. He was able to go to school and do activities of daily living with minimal supervision from his family. Symptoms of refractory seizures, hemiparesis, facial asymmetry, and intellectual disabilities along with brain imaging evidence of cerebral hemi-atrophy with compensatory calvarial thickening and subsequent hyperpneumatization is consistent with Dyke-Davidoff-Masson Syndrome (DDMS). A rare clinico-neuroradiologic condition occurring in fetal or early childhood period as a consequence of chronic brain insult. Diagnosis is established clinically with a characteristic cranial imaging finding. Hemi-spherectomy is the treatment of choice. This case will enlighten our mind as well as aid us in the prompt recognition of this uncommon syndrome with a classic clinico-radiologic presentation. Multidisciplinary intervention is essential, primarily to optimize seizure control as well as provide quality of life.
| Published in | International Journal of Clinical and Experimental Medical Sciences (Volume 9, Issue 2) |
| DOI | 10.11648/j.ijcems.20230902.11 |
| Page(s) | 21-24 |
| Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
| Copyright |
Copyright © The Author(s), 2023. Published by Science Publishing Group |
Dyke-Davidoff-Masson Syndrome (DDMS), Filipino, Adolescent
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APA Style
Lalaine Villaflor-Oida, Rowena Cabradilla, Michelle Sy, Alejandro Bimbo Diaz, Maria Antonia Aurora Valencia. (2023). Dyke-Davidoff-Masson Syndrome: A Case Report in a Filipino Male Adolescent. International Journal of Clinical and Experimental Medical Sciences, 9(2), 21-24. https://doi.org/10.11648/j.ijcems.20230902.11
ACS Style
Lalaine Villaflor-Oida; Rowena Cabradilla; Michelle Sy; Alejandro Bimbo Diaz; Maria Antonia Aurora Valencia. Dyke-Davidoff-Masson Syndrome: A Case Report in a Filipino Male Adolescent. Int. J. Clin. Exp. Med. Sci. 2023, 9(2), 21-24. doi: 10.11648/j.ijcems.20230902.11
AMA Style
Lalaine Villaflor-Oida, Rowena Cabradilla, Michelle Sy, Alejandro Bimbo Diaz, Maria Antonia Aurora Valencia. Dyke-Davidoff-Masson Syndrome: A Case Report in a Filipino Male Adolescent. Int J Clin Exp Med Sci. 2023;9(2):21-24. doi: 10.11648/j.ijcems.20230902.11
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Download@article{10.11648/j.ijcems.20230902.11,
author = {Lalaine Villaflor-Oida and Rowena Cabradilla and Michelle Sy and Alejandro Bimbo Diaz and Maria Antonia Aurora Valencia},
title = {Dyke-Davidoff-Masson Syndrome: A Case Report in a Filipino Male Adolescent},
journal = {International Journal of Clinical and Experimental Medical Sciences},
volume = {9},
number = {2},
pages = {21-24},
doi = {10.11648/j.ijcems.20230902.11},
url = {https://doi.org/10.11648/j.ijcems.20230902.11},
eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijcems.20230902.11},
abstract = {A previously well young Filipino boy presented with prolonged recurrent left focal to bilateral seizure. He was born of a non-consanguineous marriage, home-delivered vaginally, full term with no perinatal complications. He had normal growth and developmental milestones until at the age of 7 months when he developed febrile status epilepticus. Since then, he was left with residual left hemiplegia, dysarthria, cognitive delay and recurrent seizures occurring twice daily. He was poorly compliant on multiple anti-seizure medications. He was able to go to school and do activities of daily living with minimal supervision from his family. Symptoms of refractory seizures, hemiparesis, facial asymmetry, and intellectual disabilities along with brain imaging evidence of cerebral hemi-atrophy with compensatory calvarial thickening and subsequent hyperpneumatization is consistent with Dyke-Davidoff-Masson Syndrome (DDMS). A rare clinico-neuroradiologic condition occurring in fetal or early childhood period as a consequence of chronic brain insult. Diagnosis is established clinically with a characteristic cranial imaging finding. Hemi-spherectomy is the treatment of choice. This case will enlighten our mind as well as aid us in the prompt recognition of this uncommon syndrome with a classic clinico-radiologic presentation. Multidisciplinary intervention is essential, primarily to optimize seizure control as well as provide quality of life.},
year = {2023}
}
TY - JOUR T1 - Dyke-Davidoff-Masson Syndrome: A Case Report in a Filipino Male Adolescent AU - Lalaine Villaflor-Oida AU - Rowena Cabradilla AU - Michelle Sy AU - Alejandro Bimbo Diaz AU - Maria Antonia Aurora Valencia Y1 - 2023/05/10 PY - 2023 N1 - https://doi.org/10.11648/j.ijcems.20230902.11 DO - 10.11648/j.ijcems.20230902.11 T2 - International Journal of Clinical and Experimental Medical Sciences JF - International Journal of Clinical and Experimental Medical Sciences JO - International Journal of Clinical and Experimental Medical Sciences SP - 21 EP - 24 PB - Science Publishing Group SN - 2469-8032 UR - https://doi.org/10.11648/j.ijcems.20230902.11 AB - A previously well young Filipino boy presented with prolonged recurrent left focal to bilateral seizure. He was born of a non-consanguineous marriage, home-delivered vaginally, full term with no perinatal complications. He had normal growth and developmental milestones until at the age of 7 months when he developed febrile status epilepticus. Since then, he was left with residual left hemiplegia, dysarthria, cognitive delay and recurrent seizures occurring twice daily. He was poorly compliant on multiple anti-seizure medications. He was able to go to school and do activities of daily living with minimal supervision from his family. Symptoms of refractory seizures, hemiparesis, facial asymmetry, and intellectual disabilities along with brain imaging evidence of cerebral hemi-atrophy with compensatory calvarial thickening and subsequent hyperpneumatization is consistent with Dyke-Davidoff-Masson Syndrome (DDMS). A rare clinico-neuroradiologic condition occurring in fetal or early childhood period as a consequence of chronic brain insult. Diagnosis is established clinically with a characteristic cranial imaging finding. Hemi-spherectomy is the treatment of choice. This case will enlighten our mind as well as aid us in the prompt recognition of this uncommon syndrome with a classic clinico-radiologic presentation. Multidisciplinary intervention is essential, primarily to optimize seizure control as well as provide quality of life. VL - 9 IS - 2 ER -
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